Feokromocytom
Feokromocytom er en svulst som utgår fra binyremargen og som produserer økt mengde katekolaminer. Behandlingen er forebygging av komplikasjoner og fjerning av svulsten gjennom operasjon med kikkehullsteknikk.

Sist oppdatert:
3. jan. 2019
Hva er feokromocytom?

Binyrene befinner seg ved øvre pol av begge nyrene. Binyrene er hormonkjertler som produserer flere typer hormoner. Binyremargen produserer hormonene adrenalin, noradrenalin og dopamin, som på fagspråket ofte omtales som katekolaminer.
Et feokromocytom er en katekolaminproduserende svulst som utgår fra binyremarg. Tilsvarende svulstvev kan også finnes i nerveknuter (ganglier) utenfor binyrene, og kalles da paragangliomer. Eventuelle paragangliomer finnes vanligvis i bukhulen. Svulstene i binyremargen (feokromocytom) utgjør 80-85% og paragangliomer 15-20%. Siden det er samme typer svulster omtales de ofte samlet, og i engelskspråklig litteratur kalles de ofte PPGL.
Feokromocytomer og paragangliomer er sjeldne svulster. De er årsak til 0,1-0,6 prosent av alle tilfeller med høyt blodtrykk (hypertensjon). Diagnosen stilles oftest i 40-50 årene, men en arvelig form diagnostiseres ofte før 40-årsalderen. Opptil 10 prosent av feokromocytomer er ondartede svulster.
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Dette dokumentet er basert på det profesjonelle dokumentet Feokromocytom . Referanselisten for dette dokumentet vises nedenfor
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